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Myasthenia gravis, neonatal or infantile (infantile myasthenia gravis; neonatal myasthenia gravis)


Myasthenia Gravis, Neonatal or Infantile (Infantile Myasthenia Gravis; Neonatal Myasthenia Gravis)

General: Occurs in newborn of myasthenic mother; caused by compound in circ 131j96b ulation received through placenta (see Erb-Goldflam Syndrome).

Ocular: Transient diplopia; ptosis of upper eyelids; internuclear ophthalmoplegia.

Clinical: Excessive fatigue musculature; symptoms appear and increase as day progresses; expressionless face; sagging jaw; sucking, swallowing, and respiratory difficulties.



Jay WM, et al. Internuclear ophthalmoplegia with downshoot in myasthenia gravis. J Clin Neuro-Ophthalmol 1987; 7:74.

Magalini SI, Scrascia E. Dictionary of Medical Syndromes, 2nd ed. Philadelphia: JB Lippincott, 1981,577.

Papazian O. Transient neonatal myasthenia gravis. J Child Neurol 1992; 7:135-l41.

Stickroot FL, et al. Myasthenia gravis occurring in an infant born of a myasthenic mother. J Am Med Assoc 1942; 120: 1207-l209.




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