Tilted disk syndrome 1

General: Relatively common congenital anomaly (l% to 2% of the 515c25f population) consisting of inferonasal 'tilting' of the disk, with the upper and temporal portion of the disk laying anterior to the inferonasal portion.

Ocular: 'Tilting' of the disk with associated findings of an obliquely directed long axis of the disk, inferonasal crescent, posterior staphyloma of the affected inferonasal region of the fundus, and upper and temporal emergence of the retinal vessels rather than the nasal (situs inversus); lenticular astigmatism.

Clinical: Patients tend to have myopic astigmatism and superotemporal or bitemporal visual field depression; patients are at increased risk for retinal serous detachment.

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