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Susac syndrome 1


Susac Syndrome 212e46c 212e46c 212e46c 212e46c 212e46c 212e46c 1

General: Rare; unknown origin; characterized by the triad of encephalopathy, fluctuation hearing loss and visual loass resulting from microangiopathy of the brain, cochlea and retina.

Ocular: Cotton wool spot; central retinal vein occlusion;



Clinical: Hearing loss; encephalopathy

Gross M, Banin E, Eliashar R, et al. Susac syndrome. Otol Neurotol 2004; 25: 470-473.

Xu MS, Tan CB, Umapathi T, et al. Susac syndrome: serial diffusion-weighted MR imaging. Magn Reson Imaging 2004; 22: 1295-




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