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Rebeitz-kolodny-richardson syndrome


Rebeitz-Kolodny-Richardson Syndrome

General: Etiology unknown; possibly metabolic failure at cellul 757j93h ar level; occurs in late middle age; neural achromasia with corticodentatonigral degeneration.

Ocular: Paralysis of ocular muscles.

Clinical: Clumsiness, slowness of movement of left limbs; severe impairment in control of muscular movements; postural abnormalities; tremor; severe contractures; dysphagia; speech impairment; Babinski sign.



Magalini SI, Scrascia E. Dictionary of Medical Syndromes, 2nd ed. Philadelphia: JB Lippincott, 1981.

Rebeitz JJ, Kolodny H, Richardson EP. Corticodentatonigral degeneration with achromasia. Arch Neural 1968; 18:20-33.




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