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Raeder syndrome (paratrigeminal paralysis; horton headache; histamine cephalalgia; ciliary neuralgia; cluster headache; periodic migrainous neuralgia)


Raeder Syndrome (Paratrigeminal Paralysis; Horton Headache; Histamine Cephalalgia; Ciliary
Neuralgia; Cluster Headache; Periodic Migrainous Neuralgia) 545g67f 545g67f 545g67f 545g67f

General: Interruption of sympathetic fibers about the carotid artery and involvement of the fifth nerve; meningioma and aneurysm of the internal carotid artery most frequent causes; prominent in males; possible pathogenetic mechanism of this condition is an ischemic injury of the gasserian ganglion.

Ocular: Mild enophthalmos; mild ptosis (unilateral); epiphora; scotoma possible; hypotonia; unilateral miosis; increased tear secretion; periocular pain; Homer syndrome.

Clinical: Facial pain; occasionally weakness of the jaw muscles; headaches (V-region); hypertension; associated inflammatory processes are not infrequent.

Boniuk M, Schlezinger NS. Raeder's paratrigeminal syndrome. Am J Ophthalmol 1962; 54: 1074.



Coppeto JR. Migraine and other head pains. In: Albert DM, Jakobiec FA, eds. Principles and Practice of Ophthalmology, vol. IV Philadelphia: WB Saunders, 1994:2694.

Desai BT, et al. Raeder's syndrome. Ann Ophthalmol 1975; 7:1082-l084.

Fraunfelder FT, Roy FH. Current Ocular Therapy. 5th ed. Philadelphia: WB Saunders, 2000.

Grimson BS, Thompson S. Raeder's syndrome: a Clinical review. Surv Ophthalmol 1980; 24:199-210.

Lederman RJ. Fibromuscular dysplasia of the internal carotid artery. A cause of Raeder's paratrigeminal syndrome. Neurology 1976; 26:353.

Raeder JG. 'Paratrigeminal' paralysis of oculo-pupillary sympathetic. Brain 1924; 47:149.

Riley FC Jr, Moyer NJ. Oculosympathetic paresis associated with cluster headaches. Am J Ophthalmol 1971; 72: 763-768.




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