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Nieden syndrome (telangiectasia-cataract syndrome) 8


Nieden Syndrome (Telangiectasia-Cataract Syndrome) 444g67e 444g67e 444g67e 8

General: Etiology unknown; familial occurrence; onset from birth.

Ocular: Sparse eyebrows; glaucoma; dyscoria; defects of iris mesenchyme; bilateral cataract (cortical or mature).

Clinical: Telangiectasia of face and upper extremities; pigmentary changes of the neck; thick, atrophic skin; heart enlargement; congenital valvular defect.



Geeraets WJ. Ocular Syndromes, 3rd ed. Philadelphia: Lea & Febiger, 1976.

Nieden A. Cataractbildung bei Teleangiectatischer Ausdehnung der Capillaren der Ganzen Gesichtshaut. Zentbl Parkt Augenheilkd 1887; 11:353.

Petersen HP. Telangiectasis and cataract. Acta Ophthalmol 1954; 32:565.




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