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Mikulicz-radecki syndrome (mikulicz syndrome; dacryosialoadenopathy; mikulicz-sjgren syndrome)


Mikulicz-Radecki Syndrome (Mikulicz Syndrome; Dacryosialoadenopathy; Mikulicz-Sjgren
Syndrome) 737d31h 737d31h 737d31h 737d31h 737d31h 737d31h 737d31h

General: Not an individual disease but a manifestation of tuberculosis, syphilis, leukemia, lymphosarcoma, sarcoidosis, Hodgkin disease, mumps, Waldenstrm macroglobulinemia, or lymphoma; exhibits a chronic course with frequent recurrences; milder form of Sjgren syndrome (see Schaumann Syndrome).

Ocular: Bilateral painless enlargement of lacrimal glands with bulging of upper lid; decreased or absent lacrimation; conjunctivitis; uveitis; optic atrophy; optic neuritis; phlyctenules; keratoconjunctivitis; dacryoadenitis; retinal candlewax spots; periphlebitis.

Clinical: Symmetrical, perhaps marked, enlargement of salivary glands; dryness of mouth and pharynx; hoarseness; neurologic complications.

Meyer D, et al. Differential diagnosis in Mikulicz's syndrome, Mikulicz's disease, and similar disease entities. Am J Ophthalmol 1971; 71:516-524.

von Mikulicz-Radecki J. Ueber eine Eigenartige Symmetrische Erkrankung der Thranen und Mundspeicheldrusen. Beitr Chirurg Festschr Gewid T Billroth Stuttgart




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