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Macular Halo Syndrome

General: Probably variant of Niemann-Pick disease; major differences are the ocular lesion described as macular halo with a granular appearance instead of the classic cherry-red spot and the lack of major visual symptoms.



Ocular: Crystalloid opacities of foveolae; granular macula; macular halo.

Clinical: Hepatosplenomegaly; hyperlipidemia; histiocytes of bone marrow, spleen, and liver.

Cogan DG, Tedermann DD. Retinal involvement with reticuloendotheliosis of unclassified type. Arch Ophthalmol 1964; 71:489-491.

Cogan DG, et al. Macular halo syndrome. Arch Ophthalmol 1983; 101:1698-l700.




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