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Kasabach-merritt syndrome (capillary angioma-thrombocytopenia; hemangioma-thrombocytopenia; thrombocytopenia purpura-hemangioma) 6


Kasabach-Merritt Syndrome (Capillary Angioma-Thrombocytopenia; Hemangioma-Thrombocytopenia; Thrombocytopenia Purpura-Hemangioma) 6

General: Angioma causing sequestration of platelets and platelet deficiency.

Ocular: Capillary hemangiomas of the orbit; retinal detachments.

Clinical: Extraorbital hemangiomas found on trunk, extremities, and palate or in subglottic space; thrombocytopenia; found in infants; purpura and bleeding.



Kasabach HH, Merritt KK. Capillary hemangioma with extensive purpura: report of a case. Am J Dis Child 1940; 59: 1063-l 070.

Kelsch RD. Kasabach-Merritt syndrome: a case report and literature review. Compendium 1994; 15:590-598.

Lambert SR, et al. Serous retinal detachments in thrombotic thrombocytopenic purpura. Arch Ophthalmol 1985; 103: 1172-l174.




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