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Annette von droste-hulshoff syndrome


Annette Von Droste-Hulshoff Syndrome

General: Premature birth; pseudo strabismus due to macular ectopia in retinopathy of prematurity.

Ocular: Myopia; retinal detachment; negative and positive angle kappa; esotropia; temporal macular ectopia; chorioretinal colobomata; falciform folds; persistent hyaloids artery; abnormal position of blind spot; epicanthus; telecanthus; blepharophimosis; hypertelorism; asymmetrical orbits; exophthalmos; enophthalmos.



Clinical: Face turn; angioma; neoplasia.

Alfieri MC, et al. The Annette Von Droste-Hulshoff syndrome, pseudostrabismus due to macular ectopia in retinopathy of prematurity. Ophthalmic Paediatr Genet 1988; 9:13-l6.

Myer-Schweckerath G. Dos Annette Von Droste-Hulshoff syndrome. Klin Monatsbl Augenheilk 1984; 184:574.





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