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Uyemura syndrome (fundus albipunctatus with hemeralopia and xerosis)


Uyemura Syndrome (Fundus Albipunctatus with Hemeralopia and Xerosis)

General: Rare; resembles retinitis punctata albescens, 858g63i fundus albipunctatus, and congenital idiopathic night blindness or Oguchi disease; avitaminosis A; affects both sexes.

Ocular: Night blindness; conjunctival xerosis; Bitot spots; white spots on the fundus.



Clinical: None.

Krill AE, Martin D. Photopic abnormalities in congenital stationary nightblindness. Invest Ophthalmol 1971; 10:625.

Uyemura M. Uber eine Merkwurdige Augenhintergrundsveranderung bei zwei Fallen von Idiopathischer Hemeralopie. Klin Monatsbl Augenheilkd 1928; 81:471.

Venkataswamy G. Ocular manifestations of vitamin A deficiency. Br J Ophthalmol




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