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Diseases

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Shamberg disease 1


Shamberg Disease 1

General: Common benign skin disorde 616g67g r; self-limiting cutaneous vasculitis.

Ocular: Discrete foci of retinal periphlebitis associated with localized intraretinal hemorrhages and exudates; retinal and cutaneous vasculitides wax and wane concurrently; retinal vasculitis is self-limiting cause of visual disturbance and requires no therapy.



Clinical: Purpuric, erythematous patches appear on trunk and extremities; mononuclear perivascular infiltrate of involved skin.

Bedrick JJ, et al. Retinal vasculitis in Shamberg's disease. Ophthalmology 1982; 89:188.




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