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Nothnagel syndrome (ophthalmoplegia-cerebellar ataxia syndrome) 8


Nothnagel Syndrome (Ophthalmoplegia-Cerebellar Ataxia Syndrome) 8

General: Lesion of superior cerebellar peduncle, red nucleus, and emerging oculomotor fibers, such as pineal tumor, or tumor or vascular disturbance in corpora quadrigemina or vermis cerebelli (see Bruns Syndrome).

Ocular: Oculomotor paresis; gaze paralysis most frequently upward, combined with some degree of internal or external ophthalmoplegia.



Clinical: Cerebellar ataxia; poor upper extremity movements; neoplasia; infarction; midbrain lesion.

Magalini SI, Scrascia E. Dictionary of Medical Syndromes, 2nd ed. Philadelphia: JB Lippincott, 1981.

Nothnagel CWH. Topische Diagnostik der Gehirnkrankheiten. Berlin: A. Hirschwald, 1879:220.




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