Junius-kuhnt syndrome (kuhnt-junius disease; macular senile disciform degeneration [i]; macula lutea juvenile degeneration [2]) 6

General: Onset in advanced age or in juvenile period; etiology unknown; possible autosomal dominant or recessive inheritance.

Ocular: Impairment of central vision; central scotoma; atrophic macular degeneration surrounded by retinal hemorrhages, resulting in mountlike lesion; exudative and atrophic reaction with deposit in and about macula.

Clinical: None.

Deutman AF. Hereditary dystrophies of the central retina and choroid. In: Winkelman JE, Crone RA, eds. Perspectives in Ophthalmology, vol. 2. Amsterdam: Excerpta Medica, 1970.

Deutman AF. Macular dystrophies. In: Ryan SJ, ed. Retina, vol. II. 2nd ed. St. Louis, Mosby, 1994.

Kimura SJ, Caygill WM, eds. Retinal diseases. Philadelphia: Lea & Febiger, 1966.

Magalini SJ, Scrascia E. Dictionary of Medical Syndromes, 2nd ed. Philadelphia: JB Lippincott, 1981:440.