Arndt-Gottron Syndrome (Scleromyxedema) 414e45e 414e45e 414e45e 414e45e
General: Etiology unknown; rare cutaneous disease of hyaluronic acid deposits in dermis; variant of lichen myxedematosus (papular mucinosis); progressive disease commonly involving the face, neck, upper trunk, forearms, and hands, producing thickening of the skin with overlying fine papules.
Ocular: Corneal opacities of amyloid deposits; thickening of eyelids; lagophthalmos; ectropion; thickened eyebrow or eyelid skin; corneal opacities.
Clinical: Exaggerated facial folds impair opening of the mouth; flexion contractures from poor joint mobility; erythema; scaling of skin; phimosis; urethral stenosis.
Davis ML, et al. Ophthalmic findings in scleromyxedema. Ophthalmology 1994; 101:252-255.
Goldin HM, et al. Scleromyxedema with corneal deposits. Ophthalmology 1987; 94:1334-l337.
Pusateri TJ, et al. Corneal manifestations of scleromyxedema. Ophthalmology 1987; 94:510-513.
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